Pulmonary sarcoidosis in a preschool patient.

Pediatr Pulmonol

Respiratory Department, Royal Children's Hospital, Melbourne, Australia.

Published: December 2015

Sarcoidosis is a rare disease, especially in the preschool age group where it usually presents with eye, joint, and skin involvement sparing the lungs. Multiple treatment regimes have been described with oral prednisolone being the usual first line treatment. We describe a case of a 4-year-old boy presenting with pulmonary sarcoidosis with no other organ involvement. The child was successfully managed with pulse intravenous methylprednisolone followed by oral prednisolone and has had a good outcome. This case reports a rare presentation of preschool sarcoidosis as well as the novel and successful use of pulse methylprednisolone in paediatric pulmonary sarcoidosis.

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http://dx.doi.org/10.1002/ppul.23228DOI Listing

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