This case report describes the simultaneous manifestation of acute necrotizing encephalopathy in 2 consanguineous patients after infection with influenza B based on the autosomal dominant missense mutation of the RANBP2-gene. Differential diagnosis of acute encephalopathy, clinical and radiological clues, and treatment strategies are outlined.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4473106PMC
http://dx.doi.org/10.1093/ofid/ofv013DOI Listing

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