Portal cavernoma cholangiopathy.

J Clin Exp Hepatol

Service d'hépatologie, Hôpital Beaujon, HUPNVS, APHP, Université Paris Diderot, INSERM CRI, 100 Boulevard Leclerc, 92110 Clichy-la-Garenne, France.

Published: February 2014

Download full-text PDF

Source
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4244830PMC
http://dx.doi.org/10.1016/j.jceh.2014.02.002DOI Listing

Publication Analysis

Top Keywords

portal cavernoma
4
cavernoma cholangiopathy
4
portal
1
cholangiopathy
1

Similar Publications

Background: Chronic total occlusion (CTO) of the portal vein is one of the main causes of portal hypertension, which may result in life-threatening complications often managed by interventional radiology (IR). The aim of this study is to report the innovative experience with percutaneous revascularization therapy in the management of portal vein CTO in paediatric and adult patients.

Materials And Methods: From January 2020 to December 2023 consecutive paediatric and adult patients with severe portal hypertension resulting from portal vein CTO who underwent attempts at percutaneous recanalization were retrospectively reviewed.

View Article and Find Full Text PDF

Portal cavernoma cholangiopathy (PCC), also known as portal biliopathy, refers to biliary duct abnormalities caused by extrahepatic portal vein obstruction (EHPVO) and subsequent cavernous transformation of the portal vein. Pseudotumoral portal cavernoma is a specific subtype of PCC characterized by the presence of numerous thin collateral veins that mimic the sheath of the common bile duct (CBD). We present a case of a 42-year-old women with pseudotumoral portal cavernoma secondary to portal vein thrombosis, a complication of myeloproliferative disorder.

View Article and Find Full Text PDF

Management of portal vein thrombosis in candidates for liver transplant.

Liver Transpl

November 2024

Barcelona Hepatic Hemodynamic Laboratory, Liver Unit, Hospital Clínic, Clínic Barcelona, Health Care Provider of the European Reference Network on Rare Liver Disorders (ERN-RareLiver), CSUR Centro de referencia del Sistema Nacional de Salud en Enfermedad Hepática Compleja. Barcelona, Spain.

Portal vein thrombosis (PVT) is a frequent event among patients with advanced liver disease, with a prevalence reaching up to 26% in those awaiting liver transplantation (LT). Extensive thrombosis affecting the mesenteric vein confluence correlates with increased morbidity and mortality post-LT, particularly when it impedes physiological anastomosis or contraindicates the LT. Current guidelines advocate for routine PVT screening in all potential liver transplant candidates and prompt treatment upon detection.

View Article and Find Full Text PDF
Article Synopsis
  • Adult diffuse hepatic hemangiomatosis (DHH) is a very rare condition, and this case is the largest reported instance involving both liver lobes with no extrahepatic issues.
  • A 51-year-old man was treated for symptoms like abdominal swelling and difficulty breathing, leading to the discovery of a massive liver lesion determined to be 35.1 × 32.1 × 14.1 cm through imaging and biopsy.
  • The case provides valuable insights into DHH's clinical presentation and imaging characteristics, aiding in understanding this uncommon disease and assisting in the patient's ongoing care and potential liver transplant evaluation.
View Article and Find Full Text PDF

Portal cavernoma cholangiopathy treated with living donor liver transplantation: a case report and review of the literature.

Clin J Gastroenterol

December 2024

Division of Gastroenterological, General and Transplant Surgery, Department of Surgery, Jichi Medical University, 3311-1 Yakushiji, , Shimotsuke city, Tochigi, 329-0498, Japan.

Portal cavernoma cholangiopathy (PCC) is a complex condition associated with portal hypertension, particularly in patients with extrahepatic portal vein obstruction (EHPVO). Herein, we present a case of liver failure with PCC in a 55-year-old male successfully treated with living-donor liver transplantation (LDLT). The patient had a history of gastrointestinal bleeding and recurrence of cholangitis.

View Article and Find Full Text PDF

Want AI Summaries of new PubMed Abstracts delivered to your In-box?

Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!