Ebstein's anomaly (EA) is a rare congenital malformation, characterized by an apical displacement and dysplasia of the septal leaflet of the tricuspid valve with a right ventricular atrialization compromising its function. This malformation includes electrical conduction abnormalities, and very rarely ventricular arrhythmias. We report the case of a 22-year-old male, presenting with dizziness and palpitations. The electrocardiogram showed a sustained monomorphic ventricular tachycardia (SMVT). The presentation of the disease with ventricular tachycardia associated with hemodynamic instability is extremely rare. We placed a surgical implantable cardiac defibrillator when the diagnosis of EA, SMVT, and right ventricular systolic impairment was confirmed.
Download full-text PDF |
Source |
|---|---|
| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4362168 | PMC |
Publication Analysis
Top Keywords
Similar Publications
Vericiguat in patients with heart failure and implantable cardioverter-defibrillator.
Drugs Context
March 2025
Cardiology Department, Arrhythmia Unit, University Hospital La Paz, Madrid, Spain.
Background: This analysis assesses the effectiveness and tolerability profile of vericiguat in patients with heart failure with reduced ejection fraction (HFrEF) and implantable cardioverter-defibrillator, with an emphasis on the emergence of ventricular arrhythmias.
Methods: Retrospective analysis of patients with HFrEF and implantable cardioverter-defibrillator who started treatment with vericiguat in daily clinical practice in a tertiary university hospital in Spain.
Results: The study population comprised 14 patients treated since January 2023.
Point-of-Care Ultrasound in Early Identification of Tamponade: A Case Series.
Cureus
February 2025
Hospital Medicine, University of Michigan Health System, Ann Arbor, USA.
Cardiac tamponade is a life-threatening condition resulting from fluid accumulation within the pericardial sac, leading to impaired cardiac filling and output. Signs described in the literature, such as Beck's triad (hypotension, jugular venous distension (JVD), muffled heart sounds) or pulsus paradoxus can be absent especially in the early stages, particularly in non-trauma patients, making early diagnosis challenging. In this case series, we present three patients who developed tamponade with subtle symptoms, including shortness of breath and tachycardia, but without hypotension or other hallmark signs.
View Article and Find Full Text PDFStep-by-Step Approach to Phrenic Nerve Displacement.
J Cardiovasc Electrophysiol
March 2025
Department of Medicine, Cardiac Electrophysiology Program, Division of Cardiovascular Medicine, Hospital of the University of Pennsylvania, Philadelphia, Pennsylvania, USA.
Phrenic nerve injury, though rare, can be a serious complication of catheter ablation leading to significant morbidity. The close proximity of the phrenic nerve to the site of origin of arrhythmias may also impact the success of catheter ablation. When the phrenic nerve is near the optimal site of ablation, several techniques have been proposed to create separation between the nerve and the epicardium, including the introduction of fluid, gas, and balloons.
View Article and Find Full Text PDF"Double Capture" - a technique to differentiate narrow complex Supraventricular Tachycardias.
J Interv Card Electrophysiol
March 2025
Fiona Stanley Hospital, Perth, Australia.
Background: There are various diagnostic manoeuvres to distinguish between atrial tachycardia (AT), atrio-ventricular nodal re-entrant tachycardia (AVNRT) and orthodromic re-entrant tachycardia (ORT) when assessing a narrow complex supraventricular tachycardia (SVT) in the electrophysiology (EP) laboratory. These manoeuvres are commonly used in combination to come to a diagnosis due to the inability of a single test to be able to reliably differentiate between the arrhythmias.
Objective: To determine whether a single captured His-synchronous simultaneous extra-stimulus in the atrium and ventricle ("Double Capture") can reliably distinguish the mechanism of a narrow complex SVT.
First successful epicardial ventricular tachycardia ablation in a patient with substernal implantable cardioverter defibrillator.
Clin Res Cardiol
March 2025
Semmelweis University: Semmelweis Egyetem, Városmajor u. 68., Budapest, 1122, Hungary.
Want AI Summaries of new PubMed Abstracts delivered to your In-box?
Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!