AI Article Synopsis
- Sclerosing mesenteritis (SM) is a rare benign inflammatory disorder that affects the digestive tract's membranes and involves lymphoplasmacytic inflammation, fat necrosis, and fibrosis.
- A child with recurrent abdominal pain and fever was discovered to have an intra-abdominal mass, which was biopsied and diagnosed as SM linked to IgG4-related systemic disease.
- The patient is being treated with a low dose of prednisone, and no symptoms have recurred over a 24-month follow-up period, highlighting the need for clinicians to consider possible coexisting autoimmune disorders when diagnosing SM.
Article Abstract
Sclerosing mesenteritis (SM) is a rare, benign inflammatory disorder of unknown etiology, affecting the membranes of the digestive tract that involves lymphoplasmacytic inflammation, fat necrosis, and fibrosis of the mesentery. We report a child patient with a history of recurrent abdominal pain and fever who was found to have an intra-abdominal mass suspicious for malignancy. A tissue biopsy revealed the diagnosis of SM associated with IgG4-related systemic disease. The patient is currently maintained on 5 mg prednisone daily and no recurrence of symptoms was noted during the 24-month follow-up period. We emphasize, therefore, that SM can present clinical challenges and the presence of SM should cue clinicians to search for other coexisting autoimmune disorders that can have various outcomes.
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| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4271016 | PMC |
| http://dx.doi.org/10.4103/1319-3767.145333 | DOI Listing |
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