Foix-Chavany-Marie syndrome (FCMS) also known as bilateral anterior opercular syndrome is a form of suprabulbar palsy defined by the presence of bilateral voluntary facial, pharyngeal, lingual and masticatory paralysis with automatic-voluntary movement dissociation. We report an extremely rare case of FCMS in a patient with a unilateral left opercular lesion associated with a chronic asymptomatic contralateral cerebellar lesion. Despite intensive rehabilitation, little improvement was noticed at hospital discharge.
Download full-text PDF |
Source |
|---|---|
| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4248117 | PMC |
| http://dx.doi.org/10.1136/bcr-2014-206439 | DOI Listing |
Publication Analysis
Top Keywords
Similar Publications
A Rare Case of a Good Neurological Outcome following Traumatic Foix-Chavany-Marie Syndrome.
Case Rep Crit Care
May 2024
Department of Intensive Care Medicine, Kantonsspital Aarau, Aarau, Switzerland.
Article Synopsis
- Traumatic brain injury (TBI) can lead to serious long-term effects, such as disabilities and reduced quality of life, with complications like Pseudobulbar palsy and Foix-Chavany-Marie Syndrome (FCMS) being rare but significant outcomes.
- A 58-year-old man developed FCMS after a severe cycling accident, resulting in unique symptoms like facial and throat muscle dysfunction while preserving automatic movements.
- This case adds to the sparse knowledge on trauma-related FCMS, emphasizing the importance of early detection and comprehensive treatment for better patient recovery outcomes.
Recurrent lacunar strokes in a patient with small vessel disease: rare but not negligible cause of Foix-Chavany-Marie syndrome.
Neurol Sci
May 2024
Department of Systems Medicine, Stroke Unit, University of Tor Vergata, Rome, Italy.
Key Clinical Message: Unilateral opercular lesions can result in Foix-Chavany-Marie syndrome, which is marked by acute anarthria, automatic-voluntary movement dissociation-most notably the absence of voluntary facial and tongue movements-and a generally better prognosis. Better patient outcomes are mostly dependent on early detection, management, and rehabilitation.
Abstract: Opercular syndrome is a rare neurological disorder caused by bilateral or unilateral lesions of the operculum that result in symptoms related to speech and swallowing difficulties with dissociation of automatic-voluntary movements in affected muscles.
Corticobasal syndrome mimicking Foix-Chavany-Marie syndrome with suggested 4-repeat tauopathy by tau PET.
BMC Geriatr
December 2023
Department of Functional Neurology & Neurosurgery, Center for Integrated Human Brain Science, Brain Research Institute, Niigata University, 1-757 Asahimachi-Dohri, Niigata, 951-8585, Japan.
Article Synopsis
- Corticobasal syndrome (CBS) is a neurodegenerative disorder marked by symptoms like parkinsonism, limb apraxia, and language issues, often linked to tauopathies, while Foix-Chavany-Marie syndrome (FCMS) presents differently, featuring facial and speech difficulties, typically due to stroke or TDP-43 proteinopathy.
- A clinical case of a 68-year-old woman initially thought to have FCMS progressively developed symptoms that led to a final diagnosis of CBS, characterized by significant speech degradation and neurological signs reflective of frontal lobe dysfunction.
- Neuroimaging revealed 4-repeat tauopathy as the underlying pathology of CBS, and despite treatment efforts, the patient’s condition worsened rapidly, leading
Atypical Presentations of Foix-Chavany-Marie Syndrome (FCMS) in Stroke.
Cureus
April 2023
Neurology, Sree Mookambika Institute of Medical Science, Trivandrum, IND.
Foix-Chavany-Marie syndrome (FCMS) presents with anarthria and bilateral (B/L) central facio-linguo-velo-pharyngo-masticatory paralysis with "autonomic voluntary dissociation." The most common cause of FCMS is cerebrovascular disease, while rarer causes include central nervous system infection, developmental disorders, epilepsy, and neurodegenerative disorders. Even though this syndrome is also referred to as (B/L) anterior operculum syndrome, patients with lesion in sites other than (B/L) opercular regions also can develop the syndrome.
View Article and Find Full Text PDFWant AI Summaries of new PubMed Abstracts delivered to your In-box?
Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!