Bietti crystalline dystrophy with bilateral macular holes.

Objective: Bietti crystalline dystrophy is a rare form of tapetoretinal degeneration associated with retinal crystalline deposits. However, Bietti crystalline dystrophy is extremely unusually associated with macular hole formation. A 32-year-old man with Bietti crystalline dystrophy and bilateral macular holes is described.

Design: Case report and literature review.

Results: Clinical and angiographic features, optical coherence tomography results, electroretinographic findings, and visual evoked potentials are reported.

Conclusion: Bietti crystalline dystrophy can occur with bilateral macular holes, but the cause is unclear.