Gorlin syndrome with bilateral polydactyly: a rare case report.

Int J Clin Pediatr Dent

Assistant Professor, Department of Pedodontics and Preventive Dentistry, SCB Dental College and Hospital, Cuttack, Odisha, India.

Published: September 2013

Gorlin's syndrome is a rare disorder transmitted as an autosomal dominant trait. It is characterized by multiple disorders involving multiple systems. We present a case of 11-year-old male child presenting with multiple odontogenic keratocyst to the dental clinic. Retrograde diagnosis of Gorlin-Goltz syndrome was made after clinical and radiological investigation. How to cite this article: Acharya S, Panda S, Dhull KS, Sahoo SR, Ray P. Gorlin Syndrome with Bilateral Polydactyly: A Rare Case Report. Int J Clin Pediatr Dent 2013;6(3):208-212.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4086603PMC
http://dx.doi.org/10.5005/jp-journals-10005-1221DOI Listing

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