Angiosarcomas are exceedingly rare tumors that are often difficult to diagnose. Exceptionally unusual is the presentation of these tumors with Kasabach-Merritt Syndrome, a curious form of intratumoral coagulation that can be impossible to distinguish from intravascular coagulation, which is more common. Instant recognition of this clinical association can help making a prompt diagnosis and timely initiation of therapy.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4083672PMC
http://dx.doi.org/10.4081/rt.2014.5366DOI Listing

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