Adolescent-onset idiopathic hemifacial spasm.

Neurol India

Department of Neurosurgery, China-Japan Friendship Hospital, Beijing, China.

Published: August 2014

Aims: To study the clinical manifestations, illness-related factors and microsurgical management of adolescent-onset idiopathic hemifacial spasm.

Materials And Methods: Of the 1221 microvascular decompression procedures performed for idiopathic hemifacial spasm between March 2001 and July 2007, 16 (1.3%) were in adolescent age (≤18).

Results: Clinical manifestations in the adolescent-onset were typical, but milder when compared with late-onset. Gender, thickening and adhesion of the arachnoid membrane at the cerebellopontine angle and a small volume of posterior cranial fossa might be important illness-related factors for adolescent-onset idiopathic hemifacial spasm. Arterial compression was the main cause. Typical compression of offending arteries was observed in 14 patients. Compression of petrous bone crest was found in one patient. Immediate effective rate was 100%, and curative rate was 75%. The curative rate, effective rate and delayed resolution rate during the follow-up period (mean: 22.9 months) were 87.5%, 100% and 12.5%, respectively. There was no recurrence. The postoperative complications (2; 12.5%) included: One patient had transient moderate facial palsy and decreased hearing and one patient had transient decreased hearing and tinnitus.

Conclusions: This suggests that microvascular decompression is effective in adolescent-onset idiopathic hemifacial spasm.

Download full-text PDF

Source
http://dx.doi.org/10.4103/0028-3886.132367DOI Listing

Publication Analysis

Top Keywords

idiopathic hemifacial
20
adolescent-onset idiopathic
16
hemifacial spasm
16
clinical manifestations
8
illness-related factors
8
microvascular decompression
8
effective rate
8
curative rate
8
patient transient
8
decreased hearing
8

Similar Publications

Botulinum toxin modulates the blink reflex via the trigeminal afferent system in hemifacial spasm: an early and late-term effect.

Neurol Sci

December 2024

Department of Neurology, Section of Clinical Neurophysiology, Faculty of Medicine, Gazi University, Ankara, Turkey.

Background: There is growing evidence that botulinum neurotoxin (BoNT) can mediate changes at the central level through peripheral mechanisms, leading to alterations in central sensorimotor integration. However, the effect of BoNT on brainstem excitability in patients with hemifacial spasm(HFS) is not yet fully understood, and its long-term effects remain unknown.

Objective: This study aims to investigate the impact of BoNT on the excitability of the facial nucleus in patients with idiopathic HFS.

View Article and Find Full Text PDF
Article Synopsis
  • Harlequin syndrome (HS) is a rare condition that results in uneven flushing and sweating, often due to issues with the sympathetic nervous system. When it's linked to external damage, it's called Harlequin Sign.
  • *In a systematic review of the literature, researchers analyzed 1,538 studies, finding 8 case reports of Harlequin Sign associated with upper thoracic paravertebral lesions, primarily in middle-aged females.
  • *The study identified that symptoms like hemifacial flushing and anhidrosis were common, and while CT scans were mainly used for diagnosis, surgical intervention was only successful in resolving symptoms for a quarter of the patients.
View Article and Find Full Text PDF

Predictive nomogram for hearing deficits after microvascular decompression treatment.

Neurosurg Rev

August 2024

Department of Neurosurgery, Qingdao Hospital, University of Health and Rehabilitation Sciences (Qingdao Municipal Hospital), No.1 Jiaozhou Road, Qingdao, Shandong Province, 266011, P.R. China.

We explored the impact of brainstem auditory evoked potentials monitoring, as well as anatomical characteristics, in relation to their influence on hearing deficits. A total of 851 patients diagnosed with idiopathic hemifacial spasm underwent microvascular decompression treatment were recruited in our study. A nomogram was developed based on the regression analysis.

View Article and Find Full Text PDF

Oral Manifestations of Parry-Romberg Syndrome: A Case Report.

Cureus

July 2024

Pediatric Dentistry, Faculty of Dental Medicine of Rabat, Mohammed V University in Rabat, Rabat, MAR.

Parry-Romberg syndrome is a rare acquired disorder characterized by unilateral idiopathic progressive atrophy of the skin and soft tissues of the face, resulting in a sunken appearance. The muscles, cartilage, and underlying bony structures may also be affected. The etiology remains unclear and is based on several hypotheses.

View Article and Find Full Text PDF

Want AI Summaries of new PubMed Abstracts delivered to your In-box?

Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!