AI Article Synopsis
- Stiff-person syndrome is a rare autoimmune and neurogenic disorder, often linked to thymoma, a type of tumor in the thymus gland.
- Pure red blood cell aplasia is another disorder tied to thymoma, resulting in a deficiency of red blood cells.
- This text discusses the first known case of a patient with recurrent thymoma exhibiting both stiff-person syndrome and pure red blood cell aplasia, which improved after the tumor was surgically removed.
Article Abstract
Stiff-person syndrome (formerly known as stiff-man syndrome) is a very rare autoimmune and neurogenic disorder, thought to present as a paraneoplastic variant in association with thymoma. Pure red blood cell aplasia is also a paraneoplastic disorder associated with thymoma. Although separate cases of stiff-person syndrome and pure red blood cell aplasia have been reported, we describe here what is to our knowledge the first case of recurrent thymoma with both stiff-person syndrome and pure red blood cell aplasia. We describe the successful treatment of the neurogenic symptoms of stiff-person syndrome and the progressive anemia associated with pure red blood cell aplasia by tumor excision.
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| http://dx.doi.org/10.1016/j.athoracsur.2013.07.103 | DOI Listing |
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