Peliosis hepatis associated with hereditary haemorrhagic telangiectasia.

Gastroenterol Rep (Oxf)

Foundation IRCCS, Policlinico San Matteo, Institute of Radiology, University of Pavia, Pavia, Italy.

Published: November 2013

Hereditary haemorrhagic telangiectasia (HHT) is an autosomal, predominantly inherited disease characterized by diffuse telangiectases involving the skin, mucous membranes, lung, brain, gastrointestinal tract and liver. Peliosis hepatis is a rare, benign disorder causing sinusoidal dilatation and the presence of multiple blood-filled lacunar spaces within the liver. We report a case of an HHT patient with incidental magnetic resonance findings of focal hepatic peliosis.

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Source
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3938001PMC
http://dx.doi.org/10.1093/gastro/got021DOI Listing

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