A never previously reported association between mediastinal angiofollicular lymph node hyperplasia (ALNH) of the hyaline vascular type and mucocutaneous manifestations in a twenty-one-year-old man is described. Mucocutaneous lesions, unresponsive to medical therapy, promptly disappeared after resection of the mediastinal mass, indicating, as suggested for the plasmacell type, a close relationship between the systemic manifestations and ALNH.
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