AI Article Synopsis
- Dermoid sinus is a rare condition in both humans and dogs, characterized by an epithelial-lined fistula that can be linked to vertebral malformations, like Klippel-Feil syndrome (KFS) in humans, which involves congenital cervical vertebral fusion.
- This case report details a 1.5-year-old Dachshund with malformations in its cervical and thoracic vertebrae as well as abnormal thoracic limbs that exhibited symptoms such as neck pain and weak limbs, prompting medical examinations like CT scans.
- After surgical removal of a type IV dermoid sinus and thorough analysis, the dog showed significant recovery and remained stable without any recurring symptoms for six months post-s
Article Abstract
Background: Dermoid sinus is an uncommon epithelial-lined fistula that may be associated with vertebral malformations. In humans, Klippel-Feil syndrome (KFS) is a rare condition characterized by congenital cervical vertebral fusion and may be associated with other developmental defects, including dermoid sinus. The present case report describes an adult Dachshund with cervical and cranial thoracic vertebral malformations as well as thoracic limb malformations resembling KFS with a concurrent type IV dermoid sinus.
Case Presentation: A 1.5 year-old Dachshund with congenital thoracic limbs deformities and cervical-thoracic vertebral malformations presented with cervical hyperesthesia, rigidity of the cervical musculature and tetraparesis. Neurologic, radiographic, and computed tomography (CT) (2D, 3D, CT fistulography) examinations revealed skeletal anomalies, a dermoid sinus in the cranial thoracic region and epidural gas within the vertebral canal. Surgical resection and histopathological evaluation of the sinus tract were performed and confirmed a type IV dermoid sinus. The clinical signs progressively recovered postoperatively, and no recurrent signs were observed after 6 months of follow-up.
Conclusions: Cervical vertebral malformations associated with limbs anomalies have not been reported in dogs and may represent a condition similar to KFS in humans. KFS can occur concurrently with other congenital conditions including dermoid sinus and should be included among the complex congenital anomalies described in dogs.
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|---|---|
| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3975874 | PMC |
| http://dx.doi.org/10.1186/1746-6148-10-54 | DOI Listing |
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