AI Article Synopsis
- Gowers' intrasyringeal hemorrhage is a rare condition where bleeding occurs within a syrinx cavity, leading to severe neurological problems.
- A 39-year-old woman with a history of Chiari type I malformation and a lumbosacral syrinx experienced acute symptoms, including worsened gait and urinary issues, due to a massive hemorrhage detected via MRI.
- Following surgical removal of the hematoma, the patient's neurological function improved, highlighting the importance of recognizing this condition in syringomyelia patients with sudden deterioration.
Article Abstract
Background: Idiopathic hemorrhage in a syrinx is a rare entity known as Gowers' intrasyringeal hemorrhage. Bleeding confined to the syrinx cavity causes severe, sometimes acute, neurological deficits. We report a case of intrasyringeal hemorrhage into a preexisting lumbosacral syrinx associated with Chiari type I malformation.
Case Description: A 39-year-old female with Noonan syndrome underwent foramen magnum decompression and a cervical syrinx-subarachnoid shunt for Chiari type I malformation-associated syringomyelia 7 years ago. She presented progressive gait deterioration and acute urinary dysfunction, indicating conus medullaris syndrome. Initial magnetic resonance imaging revealed massive hemorrhage in the intrasyringeal cavity of the conus medullaris. The patient underwent surgical removal of the intrasyringeal hematoma and her neurological symptoms improved postoperatively.
Conclusion: Although Gowers' intrasyringeal hemorrhage is rare, this entity should be taken into consideration in patients with syringomyelia showing acute neurological deterioration.
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|---|---|
| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3927095 | PMC |
| http://dx.doi.org/10.4103/2152-7806.125546 | DOI Listing |
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Article Synopsis
- Gowers' intrasyringeal hemorrhage is a rare condition where bleeding occurs within a syrinx cavity, leading to severe neurological problems.
- A 39-year-old woman with a history of Chiari type I malformation and a lumbosacral syrinx experienced acute symptoms, including worsened gait and urinary issues, due to a massive hemorrhage detected via MRI.
- Following surgical removal of the hematoma, the patient's neurological function improved, highlighting the importance of recognizing this condition in syringomyelia patients with sudden deterioration.
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