AI Article Synopsis
- Pulmonary artery sarcomas (PAS) are rare tumors with a poor prognosis, making diagnosis challenging due to their nonspecific symptoms.
- Surgery is the primary treatment, as early radical resection is the only potential cure.
- A case involving an 88-year-old man who experienced syncope led to the discovery of a mass in the pulmonary artery, which was successfully removed and identified as a malignant sarcoma.
Article Abstract
Pulmonary artery sarcomas (PAS) are extremely rare and the prognosis of patients seems to be very poor. Their clinical appearance is highly nonspecific and variable, rendering the diagnosis difficult. Surgery remains the mainstay of treatment for PAS since early radical resection could offer the only chance of a potential cure. We describe the case of a 88-year old man who was admitted in the emergency department with syncope. The diagnostic study revealed a mass in the main pulmonary artery, extending into the right and left branches and occupying almost the whole of its size. The patient was successfully submitted to complete surgical excision of the mass, which revealed to be a malignant sarcoma.
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