AI Article Synopsis
- A 55-year-old woman was diagnosed with a perivascular epithelioid cell tumor in her rectum, which was successfully treated using transanal endoscopic microsurgery.
- After a year of follow-up, she remains cancer-free with no signs of tumor recurrence.
- Perivascular epithelioid cell tumors are rare mesenchymal tumors that can appear in various organs, with only 23 documented cases affecting the gastrointestinal tract, prompting a review of the existing literature on this condition.
Article Abstract
We report a case of perivascular epithelioid cell tumor arising in the rectum of a 55-year-old woman. The tumor was treated by transanal endoscopic microsurgery. After 1 year follow-up, the patient is alive with no radiologic or endoscopic evidence of recurrence. Perivascular epithelioid cell tumor is a rare mesenchymal tumor characterized by co-expression of melanocytic and smooth muscle markers. This rare tumor can arise in various organs, including the falciform ligament, uterus, uterine cervix, liver, kidney, lung, breast, cardiac septum, pancreas, prostate, thigh, and gastrointestinal tract. Perivascular epithelioid cell tumor of the gastrointestinal tract is very rare, with only 23 previously reported cases. We review the literature on perivascular epithelioid cell tumors arising in the gastrointestinal tract.
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|---|---|
| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3896964 | PMC |
| http://dx.doi.org/10.1186/1477-7819-12-12 | DOI Listing |
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