AI Article Synopsis
- Children diagnosed with growth hormone insensitivity syndrome (GHIS) show significant growth retardation despite normal growth hormone levels, along with oral issues like underdeveloped jaws and crowded teeth.
- A case study of a 9-year-old child with GHIS highlighted delayed eruption of permanent teeth and the presence of 14 unerupted supernumerary teeth.
- This is the first report of multiple supernumerary teeth in a patient with GHIS, with most of the extra teeth extracted except for three that were hard to access.
Article Abstract
Children with significant growth retardation and normal levels of growth hormone are diagnosed with growth hormone insensitivity. The main oral findings observed in patients with growth hormone insensitivity syndrome (GHIS) are underdeveloped jaws, crowded teeth and delayed eruption of permanent teeth. This manuscript describes a 9-year-old child diagnosed with GHIS, who had delayed eruption of permanent teeth and 14 unerupted supernumerary teeth. All supernumerary teeth were extracted except for two maxillary and one mandibular teeth which were difficult to identify and access. Multiple supernumerary teeth have never been reported before in patients with GHIS.
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