Case for diagnosis.

An Bras Dermatol

Department of Dermatology and Venereology, Centro Hospitalar São João, Porto, Portugal.

Published: April 2014

Ketron-Goodman disease was formerly considered a disseminated type of pagetoid reticulosis. However, according to the new classification consensus, it should be regarded as aggressive epidermotropic CD8 T-cutaneous lymphoma, cutaneous gamma/delta T-lymphoma, or tumor-stage mycosis fungoides, depending on the clinical-histological picture. This case highlights a rare and challenging presentation of Ketron-Goodman disease with an indolent presentation and evolution and good response to a low-grade treatment regimen, not fitting well into the new classification criteria.

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Source
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3798366PMC
http://dx.doi.org/10.1590/abd1806-4841.20132258DOI Listing

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