The population of adults with repaired tetralogy of Fallot (TOF) is growing, thanks to improvements in the surgical and medical management of this condition. Accordingly, late postrepair complications are important medical concerns in these individuals. Initial surgical repair of TOF typically occurs in infancy, consisting of patch repair of the ventricular septal defect (VSD) and relief of right ventricular outflow tract (RVOT) obstruction. Although patients may remain asymptomatic for several decades, the majority will have progressive pulmonic regurgitation that leads to right ventricular (RV) dilatation and functional deterioration. Other frequently seen complications include branch pulmonary artery stenosis, RVOT aneurysms, and recurrent VSDs. Cardiac computed tomography (CT) is widely available and, in some cases, is the imaging modality of choice for serial evaluation of TOF patients. CT is particularly useful when magnetic resonance (MR) imaging is contraindicated (eg, in patients with implantable cardiac devices). Unlike MR imaging, cardiac CT allows excellent visualization of endovascular stents and stent-mounted valves. Retrospective electrocardiographically gated cardiac CT can be used for accurate volumetric and functional analysis of the RV. Comprehensive serial evaluation will assist in determining the need for surgical pulmonary valve repair in the setting of progressive RV dysfunction. Three-dimensional volumetric images are useful for evaluation of stent integrity and aneurysm formation. The radiologist should be familiar with the anatomy of TOF, surgical interventions for repair, and postrepair complications encountered at follow-up imaging of these patients. By extracting the breadth of information obtained with cardiac multidetector CT, the radiologist can play an essential role in the management of adult patients with repaired TOF.
Download full-text PDF |
Source |
---|---|
http://dx.doi.org/10.1148/rg.334125114 | DOI Listing |
JACC Clin Electrophysiol
January 2025
Department of Cardiology, Boston Children's Hospital, Department of Pediatrics, Harvard Medical School, Boston, Massachusetts, USA. Electronic address:
JACC Asia
December 2024
Pediatric Cardiology and Adult CHD Unit, Fondazione G. Monasterio, CNR-Regione Toscana, Italy.
JACC Asia
December 2024
National Heart Research Institute Singapore, National Heart Centre Singapore, Singapore.
Background: Right ventricular restrictive physiology (RVRP) is a common occurrence in repaired tetralogy of Fallot (rTOF). The relationship of RVRP with biventricular blood flow components and kinetic energy (KE) from 4-dimensional (4D) flow cardiovascular magnetic resonance (CMR) is unclear.
Objectives: The purpose of this study was to investigate the association of 4D flow CMR parameters with RVRP in rTOF patients.
Can J Cardiol
January 2025
Research Center, Montreal Heart Institute, Department of Medicine, Université de Montréal, Montreal, Canada; Adult Congenital Heart Centre, Montreal Heart Institute, Université de Montréal, Montreal, Canada. Electronic address:
In congenital heart diseases (CHD) of moderate to great complexity involving the right ventricle (RV), the morphologic RV can be exposed to significant stressors across the lifespan either in a biventricular circulation in a sub-pulmonary or sub-aortic position, or as part of a univentricular circulation. These include pressure and/or volume overload, hypoxia, ischemia, and periprocedural surgical stress leading to remodeling, maladaptation, dilation hypertrophy and dysfunction. This review examines the macroscopic remodeling of the RV in various forms of CHD and explores remodeling trajectories, along with the effects of surgeries and residual lesion repair, in tetralogy of Fallot, Ebstein anomaly, congenitally corrected transposition of the great arteries, transposition of the great arteries with atrial switch surgery, and single ventricle palliated by Fontan.
View Article and Find Full Text PDFJ Clin Med
December 2024
Department of Cardiology, University Medical Center Groningen, University of Groningen, 9700 RB Groningen, The Netherlands.
Pregnant women with congenital heart disease carry a high risk of complications, especially when cardiac function is suboptimal. Increasing evidence suggests that impaired right ventricular (RV) function has a negative effect on placental function, possibly through venous congestion. We report a case series of hepatic and renal venous flow patterns in pregnant women with right ventricular dysfunction after repaired Tetralogy of Fallot (ToF), relative to those observed in normal pregnancy and preeclampsia.
View Article and Find Full Text PDFEnter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!