Multicystic biliary hamartoma of the liver.

Korean J Pathol

Department of Radiology, Research Institute of Clinical Medicine and Research Institute for Endocrine Sciences, Chonbuk National University Medical School, Jeonju, Korea.

Published: June 2013

AI Article Synopsis

  • Multicystic biliary hamartoma (MCBH) is a rare type of liver cystic nodule recently identified as a distinct hepatic lesion.
  • A case involved a 52-year-old male with a multicystic mass in segment 3 of the liver, which was successfully removed through surgery.
  • Detailed examination showed a distinctive honeycomb structure with cystic ducts and biliary-type cells, emphasizing the importance of recognizing MCBH to differentiate it from other liver tumors and understand its treatment responses.

Article Abstract

Multicystic biliary hamartoma (MCBH) is a very rare hamartomatous cystic nodule of the liver, which has recently been described as a new entity of a hepatic nodular lesion. We report a unique case of MCBH with a review of the literatures. A hepatic multicystic mass of segment 3 was detected in a 52-year-old male by abdominal computed tomography, and resection of this lesion was performed. Macroscopic examination revealed a 2.7×2.0 cm nodular mass with a multicystic honeycomb cut surface. Histologically, this lesion consisted of multiple dilated cystic ducts lined by biliary type epithelial cells, periductal glands and connective tissue, which included small amounts of hepatic parenchyma and blood vessels. Recognition of this unusual lesion is essential to avoid confusion with other cystic tumors of the liver, and to learn more about its natural history and response to treatment.

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Source
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3701824PMC
http://dx.doi.org/10.4132/KoreanJPathol.2013.47.3.275DOI Listing

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