Tracheobronchomegaly is a rare--probably congenital--disorder. Its clinical appearance is non-specific. The diagnosis is made by radiological methods. This paper describes the typical features in early and advanced stages and outlines the diagnostic approach.
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A rare cause of dyspnea: Mounier Kuhn syndrome.
Radiol Case Rep
February 2025
Central Unit of Radiology, University Hospital Center Ibn Rochd, School of Medicine and Pharmacy of Casablanca, Hassan II University, Casablanca, Morocco.
Mounier-Kuhn syndrome, also known as tracheobronchomegaly, is a rare clinical and radiological condition characterized by tracheobronchial dilatation and recurrent respiratory infections. Patients may be asymptomatic or present with severe respiratory illnesses. A CT scan is sufficient to confirm the diagnosis.
View Article and Find Full Text PDFState-of-the-art narrative review: Mounier-Kuhn syndrome and tracheobronchomegaly.
Respir Med
December 2024
New York City Health & Hospitals, Woodhull, Brooklyn, NY, 11206, USA; NYU Grossman School of Medicine, Division of Pulmonary Medicine, New York City Health and Hospitals, Woodhull, 760 Broadway, 8th Floor, Brooklyn, NY, 11206, USA. Electronic address:
Mounier-Kuhn syndrome (MKS) or tracheobronchomegaly is an uncommon disease of the central airways. It is characterized by pathological dilatation of the trachea and main bronchi and inevitably leads to recurrent respiratory infections, bronchiectasis, hospitalizations, and results in considerable morbidity and mortality. Despite numerous case reports, there is a shortage of evidence on clinical outcomes and limited data on interventions, thus presenting a significant gap in the literature.
View Article and Find Full Text PDFIntroduction: Mounier-Kuhn syndrome or tracheobronchomegaly, is a rare condition that consists of abnormal dilation of the trachea and main bronchi due to a pathological arrangement of smooth muscle fibers in this area.
Case Report: We present the case of a 46-year-old woman with poorly controlled asthma and recurrent infections, who was diagnosed with Mounier-Kuhn syndrome through a computed tomography scan revealing an unusual enlargement of the trachea with associated bronchiectasis.
Results: The diagnosis of Mounier-Kuhn syndrome is radiological, involving measurement of the trachea where a diameter >25 mm in men and >21 mm in women is observed.
Autofluorescence Imaging of Bronchoscopy in Mounier-Kuhn Syndrome: Negative Autofluorescence Sign.
Am J Respir Crit Care Med
September 2024
Clinical Research Center, NHO Kinki Chuo Chest Medical Center, Sakai, Japan.
A case report of unusual recurrent bronchopneumonia infections in Mounier-Kuhn syndrome.
Radiol Case Rep
June 2024
Department of Diagnostic Imaging, Radiology Unit, Pisa University Hospital, Pisa, Italy.
Mounier-Kuhn syndrome is a rare airway disease characterized by tracheal and bronchial dilatation, primarily affecting middle-aged men. We present a case of Mounier-Kuhn syndrome in a 40-year-old man with a history of recurrent respiratory infections since adolescence. The diagnostic journey involved a multidisciplinary approach incorporating clinical evaluation, radiological imaging, and bronchoscopy.
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