Marfan syndrome: a case report.

Case Rep Dent

Department of Pedodontics, SRM Dental College, SRM University, Chennai 600078, India.

Published: January 2013

Marfan syndrome is an autosomal dominant systemic disorder of the connective tissue. Children affected by the Marfan syndrome carry a mutation in one of their two copies of the gene that encodes the connective tissue protein fibrillin-1. Marfan syndrome affects most organs and tissues, especially the skeleton, lungs, eyes, heart, and the large blood vessel that distributes blood from the heart to the rest of the body. A case report of Marfan syndrome has been reported with oral features. The dental problems of the child were treated under general anesthesia and a one-month review showed intact stainless steel crowns' restorations and no signs of secondary caries.

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Source
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3529425PMC
http://dx.doi.org/10.1155/2012/595343DOI Listing

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