Ollier disease is a nonhereditary disorder characterized by multiple enchondromata, with a random asymmetrical distribution. We report an unusual case of massive ulcerating multiple enchondromata of the left hand of an 11-year-old male patient. A methodical approach to treating such a massive tumor burden and steps in reconstructing the hand are described. This case report demonstrates a radical expression of this disease; however, no malignancy was identified despite the aggressive and chronic nature of the disease. Unlike previously reported cases with less severe involvement, this patient did not undergo amputation, and this approach demonstrates a strategy for limb salvage not previously described. In particular, despite bony defects of 6 cm, no autograph was necessary for the reconstruction of the hand.
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http://dx.doi.org/10.1097/SAP.0b013e318255a3ce | DOI Listing |
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