The left ventricular non-compaction (spongy cardiomyopathy) is a rare, poorly known pathology. Disease according to WHO classification applies to unclassified cardiomyopathy. Clinical picture is nonspecific. Diagnosis is established by means of instrumental techniques such as echocardiography and magnetic resonance imaging. Spongy cardiomyopathy usually affects the left ventricle, right ventricular failure occurs much less frequently. We present a description of the disease in 18 years old girl with signs of myocardial infarction and non-compaction of both (left and right) ventricles.
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Left Ventricular Non-Compaction: Evolving Concepts.
J Clin Med
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Department of Cardiac, Thoracic, Vascular Sciences and Public Health, University of Padova, 35128 Padua, Italy.
Left ventricular non-compaction (LVNC) is a rare heart muscle disease defined by the presence of prominent left ventricular trabeculation, deep intertrabecular recesses, and a thin compact layer. Several hypotheses have been proposed regarding its pathogenesis, with the most recently accepted one being that compact layer and trabeculated layers develop independently according to an "allometric growth". The current gold-standard diagnostic criteria (in particular, the Petersen index non-compaction/compaction ratio > 2.
View Article and Find Full Text PDFLeft Ventricular Non-compaction Cardiomyopathy: A Report of a Rare Case From Saudi Arabia.
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Left ventricular non-compaction cardiomyopathy (LVNC) is an unusual congenital heart disease that predominantly affects the heart's left ventricle. This disease is characterized by deep intertrabecular recesses and hypertrabeculations of the myocardial wall that link with the ventricle cavity. During embryogenesis, the fetal myocardium has to undergo a compaction process, wherein the trabeculated and spongy myocardial tissue compacts into a dense, solid form.
View Article and Find Full Text PDFReply to "Non-dilated left ventricular non-compaction cardiomyopathy with systolic dysfunction is reclassified as non-dilated left ventricular cardiomyopathy with Hypertrabeculation".
Int J Cardiol
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Department of Cardiac, Thoracic and Vascular Sciences and Public Health, University of Padua, Italy. Electronic address:
Electrophysiological phenotyping of left ventricular noncompaction cardiomyopathy in pediatric populations: A systematic review.
Physiol Rep
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Department of Biomedical Sciences, College of Osteopathic Medicine, University of New England, Biddeford, Maine, USA.
Left ventricular noncompaction cardiomyopathy (LVNC) is a structural heart defect that has been associated with generation of arrhythmias in the population and is a cause of sudden cardiac death with severe systolic dysfunction and fatal arrhythmias. LVNC has gained increasing acknowledgment with increased prevalence. We conducted a systematic review of reported electrocardiogram (ECG) results for pediatric LVNC patients.
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Article Synopsis
- Left ventricular noncompaction (LVNC) is a rare congenital heart disorder that primarily affects the right ventricle, showing a spongy myocardial appearance due to incomplete compression of the heart muscle.
- A case is reported involving a 41-week female fetus who experienced sudden unexpected death during labor, where the right ventricular wall showed significant thickening and hypertrabeculation characteristic of LVNC.
- The investigation revealed that the cause of death was linked to electrical conduction dysfunction due to LVNC, emphasizing the importance of comprehensive post-mortem examinations for unexpected fetal deaths, though standard guidelines are lacking.
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