A rare presentation of familial mediterranean Fever; acute scrotum and hydrocele amyloidosis.

Background: Familial Mediterranean Fever (FMF) is a genetic disease characterized by recurrent febrile attacks and inflammation of serous membranes. Amyloidosis is frequent in untreated FMF patients and is also the most important complication of FMF. It is generally seen with renal, hepatic, gastrointestinal, spleen, testicular and thyroidal involvement.

Case Presentation: Herein, we report a case with acute scrotum and hydrocele amyloidosis as a presenting finding in a child with FMF.

Conclusion: Although the acute scrotum and scrotal swelling are not characteristic clinical features of FMF, this genetic disease should not be forgotten in the differential diagnosis of acute scrotum in patients of Mediterranean origins.