A rare case of primary otoscleroma of the middle ear.

Objective: We report an extremely rare case of primary otoscleroma.

Method: We present a case report and a review of the world literature concerning otoscleroma.

Results: An adult woman presented with chronic suppurative otitis media with tubotympanic disease and conductive hearing loss. On mastoid exploration, dark granulations were seen, which were identified as otoscleroma on histopathological examination. The patient responded well to streptomycin.

Conclusion: To the best of our knowledge, this is the first report of primary otoscleroma in the world literature. This case indicates that Frisch's bacillus can also spread to the middle ear.