Long-term follow-up on a case of untreated trigonocephaly.

Cleft Palate J

Center for Craniofacial Anomalies, University of California, San Francisco 99143-0442.

Published: January 1990

Trigonocephaly is typically treated during the second 3 months of life by metopic suture synostectomy, orbital rim advancement, and cranioplasty. The results are generally very pleasing in nonsyndromic patients. We have not, however, seen adults with residual deformity who preceded the present basic approach to treatment first described by Hoffman and Mohr (1976). Dominguez et al (1981) described 15 individuals who improved without treatment. The question that arises is whether we are treating this congenital problem unnecessarily, particularly in nonsyndromic patients. We present a 38-year-old untreated woman who still has residual signs of the deformity seen in early childhood photographs.

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http://dx.doi.org/10.1597/1545-1569(1990)027<0072:lfoaco>2.3.co;2DOI Listing

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