Spontaneously ruptured splenic aneurysm in a young patient with Ehlers-Danlos syndrome.

The authors describe a young patient with a history of type IV vascular Ehlers-Danlos syndrome (EDS) who underwent successful treatment for a spontaneous haemorrhage from a splenic artery aneurysm, and the authors would like to remind clinicians of the mortality and morbidity associated with vascular-type EDS.