Left hemitruncus with tetralogy of fallot and right aortic arch: rare survival beyond the first decade.

Pediatr Cardiol

Department of Cardiology, Chatrapati Shahuji Maharaj Medical University, King George Medical College, Chowk, Lucknow, 226003 UP, India.

Published: June 2012

AI Article Synopsis

  • Hemitruncus is a rare congenital heart defect, found alone or alongside other heart issues.
  • The report details a specific case involving left hemitruncus, tetralogy of Fallot, and a right-sided aortic arch in a patient during their early teens.
  • Diagnosis was achieved through echocardiography and confirmed by cardiac catheterization, followed by a successful surgical correction.

Article Abstract

Hemitruncus is an uncommon congenital anomaly that has been described in isolation or in association with other congenital cardiac malformations. This report describes a rare case of left hemitruncus with tetralogy of Fallot and a right-sided aortic arch. The patient presented to us in the early second decade. The diagnosis was suspected with echocardiography and confirmed with cardiac catheterization. The patient underwent successful surgical correction of the anomaly.

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Source
http://dx.doi.org/10.1007/s00246-012-0291-yDOI Listing

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