AI Article Synopsis
- - A young woman experienced rapid breathing difficulties and medical signs pointing to severe lung issues, possibly primary pulmonary hypertension or pulmonary embolism, leading to her acute heart failure.
- - She tragically died six weeks after her symptoms began.
- - An autopsy revealed that she had pulmonary veno-occlusive disease, a rare condition with around 100 documented cases previously.
Article Abstract
A young woman presented with rapidly progressive dyspnea and clinical findings strongly suggestive of primary pulmonary hypertension or possible pulmonary embolism (or both). She died of acute right-sided heart failure. A diagnosis of pulmonary veno-occlusive disease was made at autopsy. Approximately 100 cases of this disease have been reported previously in the literature. We describe a patient with a particularly florid progression of this unusual disease. Death occurred within six weeks of the onset of symptoms.
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| http://dx.doi.org/10.1378/chest.98.4.1037 | DOI Listing |
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