Persistent Mullerian duct syndrome is a rare form of male pseudohermaphroditism, characterized by the presence of the Mullerian duct structures in an otherwise phenotypically as well as genotypically normal male. We report two cases of males with cryptorchidism, and seminoma in the undescended abdominal testis along with Mullerian duct derivatives (uterus and fallopian tube).

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3193747PMC
http://dx.doi.org/10.4103/0970-1591.85451DOI Listing

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