Potter syndrome is a congenital anomaly characterised by bilateral renal agenesis, pulmonary hypoplasia, cardiac, skeletal abnormalities and maternal oligohydramnios. Here we report a case of Potter syndrome with bilateral renal agenesis, pulmonary hypoplasia and complete transposition of the great vessels, which had been identified during a post-mortem examination. Although cardiac anomalies are known to exist with Potter syndrome, complete transposition of the great vessels has not been reported in the literature.
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| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3029568 | PMC |
| http://dx.doi.org/10.1136/bcr.01.2009.1518 | DOI Listing |
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