Acinic cell carcinoma of the nasal vestibule. Report of a unique case.

Glandular tumours constitute a very small percentage of all neoplastic lesions in the nasal cavity. Only a very limited number of cases of acinic cell carcinoma (ACC) involving the nose have been sporadically reported throughout the medical literature. The clinical significance of this case report is due to its unique site. To our knowledge this report represents the only documentation of acinic cell carcinoma arising in the nasal vestibule. Unusual presentations of uncommon malignancies can pose considerable diagnostic dilemmas to both the surgeon and histopathologist. Awareness of these rarities is important to ensure the best patient care.