Newborn with persistent cloaca presenting with accessory phallic urethra and ambiguous genitalia.

Urology

Division of Pediatric Urology, McMaster Children's Hospital, McMaster University, Hamilton, Ontario, Canada.

Published: September 2011

Persistent cloaca is a rare urogenital anomaly that can pose significant challenges for adequate diagnosis and management. We describe the case of an infant girl with a cloacal malformation, having a single perineal orifice and an accessory phallic urethra, who presented with ambiguous genitalia at birth. The distal part of the accessory phallic urethra was used to create a mucosa-lined vestibule as a part of the total urogenital sinus mobilization. This technical maneuver allowed a more natural looking, and possibly functioning, vaginal introitus, improving the final cosmetic result.

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http://dx.doi.org/10.1016/j.urology.2010.12.044DOI Listing

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