Recurrent primary hyperphosphatemic tumoral calcinosis: a case report.

Background: Tumoral calcinosis (TC) is a special form of idiopathic calcinosis that affects adolescents and young adults. It is characterized by extensive nonosseous calcification, especially in the periarticular soft tissue regions of major joints.

Case: A young girl presented with recurrent subcutaneous swellings over both infrascapular regions and left hip. The patient had elevated serum phosphorus levels while the serum calcium levels were normal. The clinical and radiologic features were suggestive of TC, and the same was confirmed by cytologic and histopathologic study. Positive von-Kossa stain further confirmed that the deposits were of calcium and thus the diagnosis of TC.

Conclusion: TC is a disorder of obscure etiology with typical clinical, radiologic, cytologic and histopathologic features.