Nephrotic syndrome was diagnosed in 5 out of 14 children with IgA nephropathy. It was steroid responsive in two children. Clinical course of the disease was characterized by multiple recurrencies and variable response to steroid therapy. Periods of a complete sensitivity to prednisone were alternating with the periods of steroid-dependence, and resistance to steroids in on patient. Steroid sensitivity of the nephrotic syndrome in IgA nephropathy in childhood is rare. Therefore, the authors emphasize features of a positive prognostic value.
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