Multiple triggering in a girl with Ehlers-Danlos syndrome: case report.

J Hand Surg Am

Department of Orthopaedics and Traumatology, University of Hong Kong Medical Centre, Queen Mary Hospital, Hong Kong.

Published: October 2010

AI Article Synopsis

  • The report discusses a case involving multiple triggering in a patient with Ehlers-Danlos syndrome, suggesting that tendon degeneration and repetitive microtrauma may contribute to this condition.
  • The authors propose that the fraying of tendon fibers due to these factors can lead to triggering issues in affected patients.
  • In this particular case, a surgical approach that involved debriding the tendons rather than removing the A1 pulley resulted in a positive long-term recovery two years post-surgery.

Article Abstract

We report a case of multiple triggering associated with Ehlers-Danlos syndrome. We postulate that the propensity for tendon degeneration in Ehlers-Danlos syndrome coupled with repetitive microtrauma might lead to fraying of the tendon fibers and, consequently, triggering. Indeed, in our case, debridement of the tendons rather than resection of A1 pulley resulted in a good long-term functional outcome 2 years after surgery.

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http://dx.doi.org/10.1016/j.jhsa.2010.06.023DOI Listing

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