We present a rare case of Stewart-Treves syndrome characterized by a diffuse angiosarcoma of the leg in a 22-year-old man with a history of chronic lymphedema due to Klippel-Trénaunay-Weber syndrome. He underwent limb disarticulation and medical treatment with cycles of doxorubicin, oral thalidomide and sunitinib with a very good response after 12 months of follow-up.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2919991PMC
http://dx.doi.org/10.1159/000313990DOI Listing

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