Patients with rapid-onset obesity, hypothalamic dysfunction, hypoventilation, autonomic dysregulation, and neural crest tumor syndrome have poor long-term outcomes. We report a patient who was treated successfully with high-dose cyclophosphamide immunoablation. This experience offers a novel therapeutic approach and an indirect insight into the underlying pathogenesis of this syndrome.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3976575PMC
http://dx.doi.org/10.1016/j.jpeds.2010.07.006DOI Listing

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