The authors describe a clinical case of extensive olfactory neuroblastoma, comprehensive the nasal cavity, paranasal sinuses and orbit who was treated in Otolaryngology Department of the Regional Hospital in Tarnów. The patient was treated with surgery and radiotherapy without orbit exenteration and the 2--year local progression--free survival was observed. Staging system, diagnostics and therapeutic methods were analyzed. Diagnostic difficulties in olfactory neuroblastoma recognition and value of the immunohistochemical examinations were emphasized.
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