Lipofibromatous hamartoma is a rare tumor-like overgrowth of fibroadipose tissue surrounding the nerves. Most commonly, it involves the median nerve. The tumor is usually present at birth and grows very slowly. The expected age of clinical presentation is the third or fourth decades of life. The case reported here had a rapid overgrowth and presented at the age of eight. Our case is the first reported case of lipofibromatous hamartoma of the median nerve in the pediatric age group.
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Lipofibromatous Hamartoma of the Median Nerve - A Rare Condition in the Hand.
J Hand Surg Asian Pac Vol
February 2024
Hand and Reconstructive Unit, Department of Orthopaedics, Faculty of Medicine, Khon Kaen University, Khon Kaen, Thailand.
Lipofibromatous hamartoma (LFH) of the median nerve is a rare condition in the hand and often remains asymptomatic for a significant period. MRI imaging can reveal unique tumour characteristics; however, the definitive diagnosis is confirmed through a tissue biopsy. In this report, a 38-year-old male presented with a gradually growing mass on his right hand.
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J Surg Case Rep
November 2023
Orthopedic surgeon, Dammam Medical Complex, Dammam, Saudi Arabia.
Herein, we report a 48-year-old male with lipofibromatous hamartoma-induced secondary carpal tunnel syndrome, treated successfully with decompression. The patient presented to the emergency with complaints of paresthesia and oedema of the wrists. When non-invasive methods failed to ease symptoms and nerve damage became a big concern, surgical intervention was recommended.
View Article and Find Full Text PDFIntraneural lipoma of the median nerve: a case report.
Handchir Mikrochir Plast Chir
June 2024
Department of General and Hand Surgery, Pomeranian Medical University, Szczecin, Poland.
Intraneural lipomas and lipofibromas (also called lipofibromatous hamartomas) are rare, benign tumours occurring in peripheral nerves in the forearm and wrist. They usually present as asymptomatic masses, but if they are large enough, they may cause symptoms of compression neuropathy. Intraneural lipomas and lipofibromas differ with regard to anatomy and clinical behaviour: the former tumour has a well-defined capsule and most commonly occurs within the median nerve in the forearm and wrist.
View Article and Find Full Text PDF10-Year Clinical Follow-Up after Decompression of Lipofibromatous Hamartoma of the Median Nerve in a 3-Year-Old Patient: Case Report and Review of the Literature.
Children (Basel)
September 2023
Division of Hand and Microsurgery, Department of Orthopedic Surgery, Jeju National University Hospital, Jeju 63241, Republic of Korea.
Lipofibromatous hamartoma, first reported in 1953, is a rare, slowly progressive soft tissue tumor, the characteristics of which include the enlargement of the affected nerve via the epineurial and perineurial proliferation of adipose and fibrous tissues. Out of 200 previously reported cases of lipofibromatous hamartoma of the median nerve, there have been approximately 25 pediatric cases under the age of 18. Herein, we report a case of lipofibromatous hamatoma of the median nerve in a 3-year-old female patient who was surgically decompressed via carpal tunnel release and epineurolysis.
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September 2023
Rubin Institute for Advanced Orthopedics, Sinai Hospital, 2401 W Belvedere Ave, Baltimore 21215, MD, United States.
Peripheral nerve tumors of the median nerve are uncommon. We present a case of a large atypical intraneural perineurioma of the median nerve. In our case, a 27-year-old man with a history of Asperger's and Autism who was diagnosed with a lipofibromatous hamartoma of the median nerve after a biopsy and treated conservatively presented to clinic due to the slowly growing size of his lesion.
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