Tectocerebellar dysraphism is a very rare malformation associated with encephalocele and tectal deformity. This article presents tectocerebellar dysraphism with a solely vermian content of encephalocele and tectal beaking defined by magnetic resonance imaging (MRI) in a 5-month-old girl who was successfully treated surgically and demonstrated excellent prognosis at the 4-year follow-up.
Download full-text PDF |
Source |
|---|---|
| http://dx.doi.org/10.1177/0883073810367828 | DOI Listing |
Publication Analysis
Top Keywords
Similar Publications
Imaging Assessment of Re-Exploratory Repair of an Occipital Bone Defect-Associated Tectocerebellar Dysraphism via Hybrid Cranioplasty.
Pediatr Neurosurg
January 2017
Department of Radiology, Pritzker School of Medicine, University of Chicago Medical Center, Chicago, Ill., USA.
Tecto-cerebellar dysraphism with occipital encephalocele: not a distinct disorder, but part of the Joubert syndrome spectrum?
Neuropediatrics
August 2011
Division of Pediatric Radiology, The Johns Hopkins School of Medicine, Baltimore, Maryland 21287, USA.
Magnetic resonance imaging (MRI) and diffusion tensor imaging (DTI) findings in a 4-year-old child with occipital encephalocele, cerebellar vermis hypogenesis, and tectal malformation are presented. The neuroimaging findings are reminiscent of tectocerebellar dysraphism with an occipital encephalocele (TCD-OE). Additionally, elongated, thickened, and horizontally orientated superior cerebellar peduncles, an abnormally deepened interpeduncular fossa, subependymal heterotopia, and focal cortical dysplasia were noted.
View Article and Find Full Text PDFTectocerebellar dysraphism with vermian encephalocele.
J Child Neurol
November 2010
Department of Neurosurgery, Kocaeli University School of Medicine, Kocaeli, Turkey.
Tectocerebellar dysraphism is a very rare malformation associated with encephalocele and tectal deformity. This article presents tectocerebellar dysraphism with a solely vermian content of encephalocele and tectal beaking defined by magnetic resonance imaging (MRI) in a 5-month-old girl who was successfully treated surgically and demonstrated excellent prognosis at the 4-year follow-up.
View Article and Find Full Text PDFOccipital extra- and intracranial lipoencephalocele associated with tectocerebellar dysraphia.
Childs Nerv Syst
April 2004
Department of Neurosurgery, Geneva University Hospital, Rue Micheli-du-Crest 24, 1211 Genève 14, Switzerland.
Objects: Tectocerebellar dysraphism was first described by Padget and Lindenberg, together with occipital encephaloceles, cerebellar midline defects, tectal beaking, posterior kinked and displaced brainstem, and inverted cerebellum. We present a unique case of lipoencephalocele associated with tectocerebellar dysraphia and discuss the etiologies of both pathologies. The importance of the developmental comprehension of posterior fossa malformations is stressed.
View Article and Find Full Text PDFWant AI Summaries of new PubMed Abstracts delivered to your In-box?
Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!