Madelung's disease (Md) is a rare metabolic disorder which presents with multiple symmetrical nonencapsulated fatty masses situated mainly around the head, neck and nape. The main indications for Md treatment are: shortness of breath, head's movement restrictions, swallowing disorders (dysphagia), aesthetic considerations, and the fear of cancer. The standard treatment of Md is the surgical excision of pathological tissues. The disease is progressive, relapses after removal of tissue are often observed. The discussion is based on a three-year observation of Md patient operated by the authors. A good cosmetic result and symptoms subsidence were observed. There were no sings of disease recurrence.
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Article Synopsis
- Multiple symmetric lipomatosis (MLS) is a rare metabolic disorder that leads to abnormal fat deposits.
- * It is also referred to as Launois-Bensaude syndrome or Madelung disease.
- * The condition is marked by symmetrical and non-encapsulated fat accumulations in various areas of the body.
A case report on Madelung's disease and comprehensive review of the literature.
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August 2024
Department of General surgery, Bethune International Peace Hospital, No. 398, Zhongshan West Road, Qiaoxi District, Shijiazhuang, 050051, Hebei Province, China.
Background: Madelung's disease (MD), alternatively referred to as benign symmetric lipomatosis, multiple symmetric lipomatosis, or Launois-Bensaude syndrome, is an uncommon benign disorder marked by symmetric proliferation of adipose tissue in the head, neck, and torso regions.
Case Description: In this case, the patient was a female with the late middle-aged demographic, diagnosed with Type I MD. Notably, she exhibited no prior history of alcohol consumption, and there was no family history of MD.
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