We report a case of gangliocytoma at a cortical and subcortical area in the right parietal lobe. The patient had a generalized seizure at 11 years of age. The MRI shows an ill-demarcated high intensity area in T2 weighted images including an enhancing tumor of 10 mm in diameter. At first, the tumor was carefully followed up because of its small size and the surgical risk. Three years after the onset, a cyst formed at the area of the brain edema adjacent to the tumor. The cyst gradually grew to 21 mm in diameter, the edema had disappeared, and the size of the tumor became smaller (7 mm) within the next 3 years. A mural nodule, jelly-like tumor with calcification was totally removed and diagnosed as gangliocytoma. The cyst fluid was watery-clear, its wall did not contain any tumor. This is the first report of a six-year follow-up of cyst formation of gangliocytoma supporting the concept that edema is a precursor to central nervous system peritumoral cyst formation based on the similar observation of hemangioblastomas.
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Article Synopsis
- Ganglioneuroma is a rare benign tumor that can originate from the sympathetic nerves, and this case describes the second instance of such a tumor arising from the fifth cranial nerve in a pediatric patient.
- A 7-year-old boy presented with left-sided facial symptoms and seizures, and imaging revealed a significant lesion near the fifth nerve, which was confirmed to be a ganglioneuroma through histopathological analysis.
- Surgical removal of the tumor was performed successfully using a specific approach, highlighting the importance of considering ganglioneuroma in similar clinical scenarios involving lesions in the brain's Meckel's cave area.
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