Although the initial report of paraneoplastic pemphigus described individuals with mucocutaneous blistering disease, subsequent reports identified patients with lichen planus or graft versus host disease-like changes. We describe a patient with fatal autoimmune blistering disease with absence of mucous membrane lesions. The pattern of complement indirect immunofluoresence helped identify the prognosis prospectively. This case illustrates yet another presentation of the neoplasia-induced autoimmunity.
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A case of bullous disease limited to the skin illustrates the spectrum of neoplasia-induced autoimmunity.
Dermatol Online J
July 2009
Beutner Laboratories and the Departments of Microbiology and Immunology and Dermatology, School of Medicine and Biomedical Sciences, University at Buffalo, State University of New York, New York, USA.
Although the initial report of paraneoplastic pemphigus described individuals with mucocutaneous blistering disease, subsequent reports identified patients with lichen planus or graft versus host disease-like changes. We describe a patient with fatal autoimmune blistering disease with absence of mucous membrane lesions. The pattern of complement indirect immunofluoresence helped identify the prognosis prospectively.
View Article and Find Full Text PDFParaneoplastic pemphigus with clinical features of lichen planus associated with low-grade B cell lymphoma.
Int J Dermatol
May 2005
Department of Dermatology, University Hospital, P. 3000-075 Coimbra, Portugal.
Background: Neoplasia-induced lichen planus is described as a cell-mediated reaction to unknown epithelial antigens. Paraneoplastic pemphigus (PNP), characterized by the presence of a specific array of autoantibodies, probably represents a different form of presentation of the same autoimmune syndrome where the mucocutaneous expression depends on the dominant pathologic mechanism.
Methods: The authors report a case of PNP with predominant lichen planus-like lesions and review the relevant literature.
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