The omphalocele-exstrophy-imperforate anus-spinal defects (OEIS) complex was first described by Carey et al. in 1978. It constitutes a specific combination of malformations. There are very few case reports of discordant OEIS in monozygotic twins and very few reports of OEIS in association with both hypoplastic left heart and ventricular septal defect. Our case represents the fifth reported case of cardiac malformations in a fetus with OEIS complex.
Download full-text PDF |
Source |
|---|---|
| http://dx.doi.org/10.1080/15513810903202570 | DOI Listing |
Publication Analysis
Top Keywords
Similar Publications
Bladder exstrophy-epispadias-cloacal exstrophy complex: characteristics, aetiologies, and epidemiologic findings.
Afr Urol
June 2024
Division of Urology, Department of Surgery, University of Utah School of Medicine, United States of America.
Bladder exstrophy-epispadias-cloacal exstrophy complex (BEEC) is a spectrum of congenital urologic anomalies that involve the bladder, urethra, genitalia, and pelvic musculoskeletal system, and can affect urinary continence, sexual health, and fertility. BEEC includes a wide spectrum of anatomical abnormalities with different levels of severity: epispadias represents the mildest phenotype, classic bladder exstrophy (CBE) is the most common defect, and cloacal exstrophy (CE) - often referred to as omphalocele, exstrophy, imperforate anus, and spinal defects (OEIS) complex - is the most severe form. BEEC disorders cause significant health problems and affect the health-related quality of life (QoL) of affected individuals.
View Article and Find Full Text PDFA rare presentation of OEIS complex in a spontaneous dizygotic twin pregnancy: A case report and literature review.
Radiol Case Rep
January 2025
University of Sousse, Faculty of Medicine of Sousse, Sousse 4000, Tunisia.
Article Synopsis
- OEIS complex is a rare birth defect involving omphalocele, bladder exstrophy, anal imperforation, and spina bifida, likely caused by multiple factors.
- A case is reported involving a 29-year-old woman pregnant with dizygotic twins, where the condition was suspected at 22 weeks through ultrasound and confirmed with MRI.
- The study highlights the importance of prenatal imaging in diagnosing OEIS complex for better counseling and management options before and after birth.
Delphi Consensus on Diagnostic Criteria for LUMBAR Syndrome.
J Pediatr
September 2024
Department of Neurosurgery, Pennsylvania State College of Medicine, Hershey, PA.
Objective: To develop consensus on diagnostic criteria for LUMBAR syndrome, the association of segmental infantile hemangiomas that affect the Lower body with Urogenital anomalies, Ulceration, spinal cord Malformations, Bony defects, Anorectal malformations, Arterial anomalies and/or Renal anomalies.
Study Design: These diagnostic criteria were developed by an expert multidisciplinary and multi-institutional team based on analysis of peer-reviewed data, followed by electronic-Delphi consensus of a panel of 61 international pediatric specialists.
Results: After 2 Delphi rounds, a 92% or higher level of agreement was reached for each Delphi statement.
OIES complex diagnosed by in utero ultrasound a case report.
Int J Surg Case Rep
May 2024
Maternity, Mother and Child Hospital Abderrahim HAROUCHI, University Hospital IBN ROCHD of Casablanca, Morocco.
Introduction And Importance: OEIS complex is a rare and complex anomaly of the genitourinary and intestinal tract. It includes Omphalocele, Exstrophy of cloaca, Imperforate anus and Spinal defects.
Presentation Of Case: We are reporting a case of OEIS complex.
Understanding and managing a case of the omphalocele-exstrophy-imperforate anus-spinal defect complex.
J Surg Case Rep
March 2024
Department of Paediatrics, Nairobi West Hospital, Nairobi, Kenya.
The omphalocele-exstrophy-imperforate anus-spinal defects (OEIS) complex is a rare birth disorder involving a combination of gastrointestinal, musculoskeletal, renal, neural, and genitourinary system defects. We present a case report of a neonate with OEIS born by vertex spontaneous delivery to non-consanguineous parents. The major presenting defect was exstrophy of the cecum lying between two exstrophied halves of the bladder, an imperforate anus and spina bifida myelomeningocele.
View Article and Find Full Text PDFWant AI Summaries of new PubMed Abstracts delivered to your In-box?
Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!