Scimitar vein anomaly with total right-side pulmonary vein return to inferior vena cava concomitant with atresia of upper right-side pulmonary vein and secundum atrial septal defect.

Scimitar vein is the partial anomalous pulmonary venous connection usually draining lower pulmonary lobe to the inferior vena cava or right atrium. We present a scimitar vein anomaly in a 34-year-old woman with the uncommon association of a secundum type of atrial septal defect and atretic right upper pulmonary vein. She presented with increasing dyspnea for 2 months, however, she was asymptomatic in the past 10 years despite the presence of atrial septal defect. We describe its diagnostic and surgical approach.