Stewart-Bluefarb syndrome: a case report with angiographic findings.

J Dermatol

Department of Dermatology, Medical Faculty, Ege University, Bornova TR-35100, Izmir, Turkey.

Published: July 2009

Acroangiodermatitis is a group of benign, angioproliferative cutaneous disease caused by chronic venous insufficiency, acquired or congenital arteriovenous shunts and limb paralysis. Stewart-Bluefarb syndrome is the type of acroangiodermatitis which is associated with a congenital arteriovenous malformation. This is a rare syndrome characterized by cutaneous kaposiform lesions that usually onset at the second decade. In this report, a case of acroangiodermatitis associated with a congenital arteriovenous malformation, which has been diagnosed after 40 years, is described.

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http://dx.doi.org/10.1111/j.1346-8138.2009.00661.xDOI Listing

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