The occurrence of cutaneous angiolipomas and intra-abdominal retroperitoneal chemodectomas in two brothers is described. Both died from malignant dissemination of the chemodectomas. It is possible but speculative that two other brothers suffered from the same syndrome.

Download full-text PDF

Source
http://dx.doi.org/10.3109/00313027709085255DOI Listing

Publication Analysis

Top Keywords

cutaneous angiolipomas
8
familial abdominal
4
abdominal chemodectomas
4
chemodectomas associated
4
associated cutaneous
4
angiolipomas occurrence
4
occurrence cutaneous
4
angiolipomas intra-abdominal
4
intra-abdominal retroperitoneal
4
retroperitoneal chemodectomas
4

Similar Publications

Nevus lipomatosus cutaneous superficialis is a rare, benign hamartoma characterized by mature adipocyte proliferation in the dermis. It is frequently difficult to distinguish clinically from soft tissue tumors, including lipoma, neurofibroma, venous malformation, and angiolipoma. Notably, the classical form, which shows multiple and sometimes enlarged nodules, is difficult to differentiate from liposarcoma based on clinical examination, computed tomography, and magnetic resonance imaging findings.

View Article and Find Full Text PDF
Article Synopsis
  • The text discusses the cases of three women aged 35 to 42 who experienced painful dermatofibromas, with one patient on long-term immunosuppressive therapy after a liver transplant, while the others were healthy.
  • The dermatofibromas varied in size from 5 to 12 mm, exhibited different colors, and were located on the buttock, shoulder, and arm; all women reported pain that lasted several months to over a year.
  • Upon undergoing punch biopsies that removed most of the tumors, all women reported relief from pain, and the text also highlights the development of mnemonics to help clinicians remember various tender cutaneous neoplasms, including a new acrostic inspired by the book
View Article and Find Full Text PDF
Article Synopsis
  • A 70-year-old woman developed a painful, enlarging nodule on her forearm, which was found to be a subcutaneous mass after surgical excision.
  • The pathology revealed that it was an intravenous lobular capillary hemangioma (IVLCH), a rare benign tumor that typically causes discomfort but can be cured with excision.
  • The authors propose a new acronym for identifying various cause of tender skin tumors, emphasizing the need for ongoing updates in this classification to assist medical professionals in their diagnoses.*
View Article and Find Full Text PDF

We studied telocytes/CD34+ stromal cells (TCs/CD34+SCs) in pathologically affected white adipose tissue after briefly examining them in normal fat. To this aim, we reviewed pathological processes, including original contributions, in which TCs/CD34+SCs are conserved, increased, and lost, or acquire a specific arrangement. The pathologic processes in which TCs/CD34+SCs are studied in adipose tissue include inflammation and repair through granulation tissue, iatrogenic insulin-amyloid type amyloidosis, non-adipose tissue components (nerve fascicles and fibres in neuromas and hyperplastic neurogenic processes) and tumours (signet ring carcinoma with Krukenberg tumour and colon carcinoma) growing in adipose tissue, adipose tissue tumours (spindle cell lipoma, dendritic fibromyxolipoma, pleomorphic lipoma, infiltrating angiolipoma of skeletal muscle and elastofibrolipoma), lipomatous hypertrophy of the interatrial septum, nevus lipomatosus cutaneous superficialis of Hoffman-Zurhelle and irradiated adipose tissue of the perirectal and thymic regions.

View Article and Find Full Text PDF

Angiomyolipomas (AMLs) are benign tumors consisting of smooth muscle-like cells, adipocyte-like cells, and epithelioid cells. They are usually renal in origin, and extrarenal AMLs are rare. Cutaneous AMLs are even more rare.

View Article and Find Full Text PDF

Want AI Summaries of new PubMed Abstracts delivered to your In-box?

Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!